European Journal of Cardio-Thoracic Surgery, Vol 11, 588-590, Copyright © 1997 by European Association for Cardio-thoracic Surgery
Replacement of right ventricle to pulmonary artery and right atrium to right ventricle homograft after a modified Rastelli operation
AA Amirghofran and J Stark
Cardiothoracic Unit, Great Ormond Street Hospital for Children NHS Trust, London, UK.
The patient, a 17 year old boy, had undergone a Rastelli operation for
transposition of the great arteries plus ventricular septal defect and left
ventricular outflow tract obstruction at the age of 7 years. Associated
tricuspid valve stenosis was treated with insertion of a second homograft
shortly after the Rastelli operation. The patient remained symptom-free for
10 years, when he suffered femoral artery embolus. Investigation showed
severe obstruction of both conduits and biventricular dysfunction with
thrombus in the left ventricle. After embolectomy and stabilisation of his
general condition and prolonged treatment with heparin, he underwent
uneventful replacement of the two conduits. He remains well, 8 months after
the operation.